Congenital hepatic fibrosis
http://purl.obolibrary.org/obo/HP_0002612
The presence of fibrosis of that part of the liver with congenital onset. [ HPO:probinson ]
Term info
- MSH:C562378
- UMLS:C0009714
- SNOMEDCT_US:79607001
Congenital hepatic fibrosis is characterized by enlarged portal tracts with extensive fibrosis and numerous bile ductules that communicate with the bile tree. The affected area tends to be sharply demarcated from normal liver parenchyma and does not display regenerative nodules (which distinguished the condition from cirrhosis).
The presence of fibrosis of that part of the liver with congenital onset.
Excessive buildup of connective tissue and scarring of liver at birth, Congenital liver fibrosis
HP:0002612