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undifferentiated pleomorphic sarcoma

^ http://purl.obolibrary.org/obo/MONDO_0002142


An undifferentiated soft tissue sarcoma characterized by the presence of a pleomorphic malignant cellular infiltrate. It is also known as malignant fibrous histiocytoma. [ NCIT:C4247 ]

Term info

database cross reference
  • DOID:1907 (MONDO:equivalentTo)
  • ICDO:8830/3 (NCIT:C4247)
  • Orphanet:2023 (MONDO:equivalentTo)
  • GARD:0006963 (MONDO:equivalentTo)
  • NCIT:C4247 (MONDO:equivalentTo)
  • SCTID:443439001 (MONDO:equivalentTo)
  • ICD9:171.9 (MONDO:relatedTo)
  • NCIT:C114541 (MONDO:equivalentTo)
  • ONCOTREE:MFH (MONDO:equivalentTo)
  • HGNC:16982 (GARD:0006963)
  • MESH:D051677 (Orphanet:2023/e)
  • MedDRA:10025552 (Orphanet:2023/e)
  • EFO:1001972 (MONDO:equivalentTo)
Subsets

gard_rare, ordo_disease

abbreviation
UPS [ NCIT:C4247 Orphanet:2023 ]

abbreviation
MFH [ NCIT:C4247 DOID:1907 ]

closeMatch

http://identifiers.org/meddra/10025552

definition

An undifferentiated soft tissue sarcoma characterized by the presence of a pleomorphic malignant cellular infiltrate. It is also known as malignant fibrous histiocytoma.

exactMatch

http://purl.obolibrary.org/obo/DOID_1907, http://purl.obolibrary.org/obo/NCIT_C4247, http://identifiers.org/mesh/D051677, http://identifiers.org/snomedct/443439001, http://purl.obolibrary.org/obo/NCIT_C114541, http://purl.obolibrary.org/obo/Orphanet_2023

has alternative id

MONDO:0016069

has exact synonym

malignant fibrous histiocytoma, Storiform-pleomorphic MFH, Unclassified Pleomorphic sarcoma (formerly "malignant fibrous histiocytoma"), malignant fibrous histiocytoma of the soft tissue and bone, Storiform-pleomorphic fibrous histiocytoma, histiocytoma, fibrous, malignant, adult malignant fibrous histiocytoma, MFH, Storiform-pleomorphic malignant fibrous histiocytoma, fibrous histiocytoma, malignant (morphologic abnormality), undifferentiated pleomorphic sarcoma, unclassified pleomorphic sarcoma, fibroxanthosarcoma, malignant fibrous histiocytoma of soft tissue and bone, fibrous histiocytoma, malignant, adult undifferentiated pleomorphic sarcoma, Unclassified Pleomorphic sarcoma (formerly "MFH"), malignant fibrous cytoma, UPS, malignant fibroxanthoma, undifferentiated pleomorphic soft tissue sarcoma, fibroxanthosarcoma (morphologic abnormality), adult unclassified pleomorphic sarcoma

has related synonym

malignant fibrohistiocytic tumors, undifferentiated pleomorphic sarcoma/malignant fibrous histiocytoma/high-grade spindle cell sarcoma

id

MONDO:0002142

seeAlso

https://rarediseases.info.nih.gov/diseases/6963/undifferentiated-pleomorphic-sarcoma

Term relations