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chronic thromboembolic pulmonary hypertension

^ http://purl.obolibrary.org/obo/MONDO_0013024

Chronic thromboembolic pulmonary hypertension (CTEPH) is characterized by the persistence of thromboemboli in the form of organized tissue obstructing the pulmonary arteries. The consequence is an increase in pulmonary vascular resistance (PVR) resulting in pulmonary hypertension (PH) and progressive right heart failure. [ Orphanet:70591 ]

Term info

database cross reference
  • MedDRA:10068739 (Orphanet:70591/e)
  • SCTID:233947005 (MONDO:equivalentTo)
  • ICD9:415.19 (MONDO:relatedTo)
  • ICD9:416.8 (MONDO:relatedTo)
  • Orphanet:70591 (OMIM:612862)
  • UMLS:C2363973 (Orphanet:70591/e)
  • GARD:0013124 (MONDO:equivalentTo)
  • OMIM:612862 (Orphanet:70591/e)
Subsets

gard_rare, ordo_disease

abbreviation
CTEPH [ Orphanet:70591 ]

closeMatch

http://identifiers.org/meddra/10068739

definition

Chronic thromboembolic pulmonary hypertension (CTEPH) is characterized by the persistence of thromboemboli in the form of organized tissue obstructing the pulmonary arteries. The consequence is an increase in pulmonary vascular resistance (PVR) resulting in pulmonary hypertension (PH) and progressive right heart failure.

exactMatch

http://purl.obolibrary.org/obo/Orphanet_70591, http://linkedlifedata.com/resource/umls/id/C2363973, https://omim.org/entry/612862, http://identifiers.org/snomedct/233947005

has related synonym

Cteph, Dvt-negative, susceptibility to, pulmonary hypertension, chronic thromboembolic, without deep vein thrombosis, susceptibility to

id

MONDO:0013024

seeAlso

https://rarediseases.info.nih.gov/diseases/13124/chronic-thromboembolic-pulmonary-hypertension

Term relations