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non-Langerhans cell histiocytosis

^ http://purl.obolibrary.org/obo/MONDO_0015531


Group of disorders which feature accumulations of active HISTIOCYTES and LYMPHOCYTES, but where the histiocytes are not LANGERHANS CELLS. The group includes HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; SINUS HISTIOCYTOSIS; xanthogranuloma; reticulohistiocytoma; juvenile XANTHOGRANULOMA; xanthoma disseminatum; as well as the lipid storage diseases (SEA-BLUE HISTIOCYTE SYNDROME; and NIEMANN-PICK DISEASES). [ MESH:D015616 ]

Term info

database cross reference
  • GARD:0008231 (MONDO:shared-umls-xref)
  • UMLS:C0019624 (Orphanet:157987/e)
  • ICD9:288.4 (MONDO:i2s)
  • DOID:4330 (MONDO:equivalentTo)
  • Orphanet:157987 (MONDO:equivalentTo)
  • SCTID:127069007 (MONDO:equivalentTo)
  • MESH:D015616 (Orphanet:157987/e)
Subsets

disease_grouping, ordo_group_of_disorders

definition

Group of disorders which feature accumulations of active HISTIOCYTES and LYMPHOCYTES, but where the histiocytes are not LANGERHANS CELLS. The group includes HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; SINUS HISTIOCYTOSIS; xanthogranuloma; reticulohistiocytoma; juvenile XANTHOGRANULOMA; xanthoma disseminatum; as well as the lipid storage diseases (SEA-BLUE HISTIOCYTE SYNDROME; and NIEMANN-PICK DISEASES).

exactMatch

http://purl.obolibrary.org/obo/Orphanet_157987, http://identifiers.org/snomedct/127069007, http://purl.obolibrary.org/obo/DOID_4330, http://linkedlifedata.com/resource/umls/id/C0019624, http://identifiers.org/mesh/D015616

excluded subClassOf

http://purl.obolibrary.org/obo/MONDO_0017368

has exact synonym

non-Langerhans-cell histiocytosis

has related synonym

histiocytosis, non-Langerhans-cell

id

MONDO:0015531

Term relations

Subclass of: