inflammatory myofibroblastic tumor
A multinodular intermediate fibroblastic neoplasm that arises from soft tissue or viscera, in children and young adults. It is characterized by the presence of spindle-shaped fibroblasts and myofibroblasts, and a chronic inflammatory infiltrate composed of eosinophils, lymphocytes, and plasma cells. [ NCIT:P378 ]
Term info
- ONCOTREE:IMT (MONDO:equivalentTo)
- GARD:0007146 (MONDO:equivalentTo)
- MESH:D006104 (MONDO:equivalentTo)
- DOID:0050905 (MONDO:equivalentTo)
- NCIT:C6481 (MONDO:exact-label-match)
- Orphanet:178342 (MONDO:equivalentTo)
- ICDO:8825/1 (NCIT:C6481)
- UMLS:C0334121 (Orphanet:178342/e)
- MedDRA:10067917 (Orphanet:178342/e)
gard_rare, ordo_disease
http://identifiers.org/meddra/10067917
A multinodular intermediate fibroblastic neoplasm that arises from soft tissue or viscera, in children and young adults. It is characterized by the presence of spindle-shaped fibroblasts and myofibroblasts, and a chronic inflammatory infiltrate composed of eosinophils, lymphocytes, and plasma cells.
http://linkedlifedata.com/resource/umls/id/C0334121, http://purl.obolibrary.org/obo/Orphanet_178342, http://identifiers.org/mesh/D006104, http://purl.obolibrary.org/obo/NCIT_C6481, http://purl.obolibrary.org/obo/DOID_0050905
IMT, inflammatory myofibroblastic neoplasm, inflammatory myofibroblastic tumor, inflammatory fibrosarcoma, inflammatory pseudotumor
MONDO:0015798
https://rarediseases.info.nih.gov/diseases/7146/inflammatory-myofibroblastic-tumor