JSON

vasculitis

^ http://purl.obolibrary.org/obo/MONDO_0018882


Vasculitis represents a clinically heterogenous group of diseases of multifactorial etiology characterized by inflammation of either large-sized vessels (large-vessel vasculitis, e.g. Giant-cell arteritis and Takayasu arteritis), medium-sized vessels (medium-vessel vasculitis e.g. polyarteritis nodosa and Kawasaki disease), or small-sized vessels (small-vessel vasculitis, e.g. granulomatosis with polyangiitis, microscopic polyangiitis, immunoglobulin A vasculitis, and cutaneous leukocytoclastic angiitis). Vasculitis occurs at any age, may be acute or chronic, and manifests with general symptoms such as fever, weight loss and fatigue, as well as more specific clinical signs depending on the type of vessels and organs affected. The degree of severity is variable, ranging from life or sight threatening disease (e.g. BehC'et disease) to relatively minor skin disease. [ Orphanet:52759 ]

Term info

database cross reference
  • GARD:0009565 (MONDO:equivalentTo)
  • NCIT:C26912 (MONDO:exact-label-match)
  • UMLS:C0042384 (Orphanet:52759/e)
  • DOID:865 (MONDO:equivalentTo)
  • Orphanet:280369 (MONDO:mondoIsBroaderThanSource)
  • Wikipedia:Vasculitis (EFO:0006803)
  • Orphanet:52759 (MONDO:equivalentTo)
  • MESH:D014657 (Orphanet:52759/e)
  • EFO:0006803 (MONDO:equivalentTo)
  • SCTID:31996006 (MONDO:equivalentTo)
  • MedDRA:10047115 (Orphanet:52759/e)
  • MedDRA:10036023 (Orphanet:52759/e)
Subsets

disease_grouping, ordo_group_of_disorders

closeMatch

http://identifiers.org/meddra/10036023, http://identifiers.org/meddra/10047115

definition

Vasculitis represents a clinically heterogenous group of diseases of multifactorial etiology characterized by inflammation of either large-sized vessels (large-vessel vasculitis, e.g. Giant-cell arteritis and Takayasu arteritis), medium-sized vessels (medium-vessel vasculitis e.g. polyarteritis nodosa and Kawasaki disease), or small-sized vessels (small-vessel vasculitis, e.g. granulomatosis with polyangiitis, microscopic polyangiitis, immunoglobulin A vasculitis, and cutaneous leukocytoclastic angiitis). Vasculitis occurs at any age, may be acute or chronic, and manifests with general symptoms such as fever, weight loss and fatigue, as well as more specific clinical signs depending on the type of vessels and organs affected. The degree of severity is variable, ranging from life or sight threatening disease (e.g. BehC'et disease) to relatively minor skin disease.

exactMatch

http://purl.obolibrary.org/obo/Orphanet_52759, http://linkedlifedata.com/resource/umls/id/C0042384, http://identifiers.org/snomedct/31996006, http://purl.obolibrary.org/obo/NCIT_C26912, http://purl.obolibrary.org/obo/DOID_865, http://identifiers.org/mesh/D014657

has narrow synonym

systemic vasculitis

id

MONDO:0018882

narrowMatch

http://purl.obolibrary.org/obo/Orphanet_280369