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primary progressive aphasia

^ http://purl.obolibrary.org/obo/MONDO_0019806

Primary progressive aphasia (PPA) is a neurodegenerative disorder, characterized by a primary dissolution of language, with relative sparing of other mental faculties for at least the first 2 years of illness. PPA is recognized as the language variant in the frontotemporal dementia (FTD) spectrum of disorders. PPA can be classified into 3 subtypes based on specific speech and language features: semantic dementia (SD), progressive non-fluent aphasia (PNFA) and logopenic progressive aphasia (lv-PPA). [ Orphanet:95432 ]

Term info

database cross reference
  • Orphanet:95432 (MONDO:equivalentTo)
  • GARD:0008541 (MONDO:equivalentTo)
  • NCIT:C85024 (MONDO:equivalentTo)
  • EFO:0009053 (MONDO:equivalentTo)
  • UMLS:C0282513 (Orphanet:95432/e)
  • MESH:D018888 (Orphanet:95432/e)
Subsets

disease_grouping, ordo_group_of_disorders

abbreviation
PPA [ OMIM:607485 Orphanet:95432 ]

IAO 0000233

https://github.com/monarch-initiative/mondo/issues/5507

definition

Primary progressive aphasia (PPA) is a neurodegenerative disorder, characterized by a primary dissolution of language, with relative sparing of other mental faculties for at least the first 2 years of illness. PPA is recognized as the language variant in the frontotemporal dementia (FTD) spectrum of disorders. PPA can be classified into 3 subtypes based on specific speech and language features: semantic dementia (SD), progressive non-fluent aphasia (PNFA) and logopenic progressive aphasia (lv-PPA).

exactMatch

http://identifiers.org/mesh/D018888, http://purl.obolibrary.org/obo/Orphanet_95432, http://linkedlifedata.com/resource/umls/id/C0282513, http://purl.obolibrary.org/obo/NCIT_C85024

has exact synonym

PPA, Mesulam syndrome

has related synonym

primary progressive aphasia syndrome

id

MONDO:0019806

Term relations